Benjamin Shneider MD

PubMed

• A phase 2 trial of short-term intravenous N-acetylcysteine in biliary atresia after Kasai portoenterostomy.
  Sanjiv Harpavat, Kristin A Borovsky, Michael E Scheurer, Laurel Cavallo, Franca E Erhiawarie
  Hepatology Communications. 2025-07-01
• Prevalence of fibrosis in hepatic explants and biopsies from individuals with urea cycle disorders.
  Saima Ali, Aisha Nisar, Anqing Zhang, Sandesh Nagamani, Nathalie M Aceves-Ewing
  Molecular Genetics and Metabolism. 2025-06-13
• An ultrasound approach to visualize the "duct at the hilum" in infants undergoing evaluation for biliary atresia.
  Ashley M Upton, Jose A Hernandez, Benjamin L Shneider, Tebyan A Rabbani, Sridevi Devaraj
  Journal of Pediatric Gastroenterology and Nutrition. 2025-06-02

Journal Articles

• Accuracy of the Pediatric End-Stage Liver Disease Score in Estimating Pretransplant Mortality Among Pediatric Liver Transplant Candidates  
  Robert H Squires, Benjamin L Shneider, JAMA
• Bile acid pool dynamics in progressive familial intrahepatic cholestasis with partial external biliary diversion  
  J. Pediatr. Gastroenterol. Nutr, 1/1/2015
• Byler's Disease-Early natural history, A single center case series  
  J. Pediatr. Gastroenterol. Nutr, 1/1/2015
• Delta4-3-oxosteroid 5beta-reductase deficiency causing neonatal liver failure and hemochromatosis  
  J Ped, 1/1/2014
• c-Fos mediates repression of the apical sodium dependent bile acid transporter by fibroblast growth factor-19 in mice  
  Am. J. Physiol.: GI and Liver, 1/1/2014
• Effect of high dose corticosteroids following hepatoportoenterostomy on bile drainage in infants with biliary atresia: The START randomized clinical trial  
  JAMA, 1/1/2014
• Medical status of 219 children with biliary atresia surviving long-term with their native livers: Results of a North American multicenter consortium  
  J. Pediatr., 1/1/2014
• The Medication Level Variability Index (MLVI) predicts rejection, possibly due to nonadherence, in adult liver transplant recipients  
  Liver Transplantation, 1/1/2014
• A single element in the 3'UTR of the Apical Sodium-Dependent Bile Acid Transporter controls both stabilization and destabilization of mRNA  
  Biochemical Journal, 1/1/2014
• Total serum bilirubin predicts fat-soluble vitamin deficiency better than serum bile acids in infants with biliary atresia  
  J. Pediatr. Gastroenterol. Nutr, 1/1/2014
• Liver transplantation for pediatric metabolic disease  
  Molec. Genet. Metabol, 1/1/2014
• Autosomal recessive polycystic kidney disease: Report of an international clinical care conference  
  J. Pediatr, 1/1/2014
• King's College Hospital criteria for nonacetaminophen induced acute liver failure in an international cohort of children  
  J. Pediatr, 1/1/2013
• Intravenous N-acetylcysteine in pediatric patients with non-acetaminophen acute liver failure: A placebo-controlled clinical trial  
  Hepatology, 1/1/2013
• Phospholipase D2 mediates signaling by ATPase Class I Type 8B Membrane 1  
  J. Lipid Res, 1/1/2013
• Liver Transplantation for children with biliary atresia in the PELD era: Role of insurance status  
  Liver Transplantation, 1/1/2013
• Extra-hepatic anomalies in infants with biliary atresia: Results of a large prospective North American multi-center study  
  Hepatology, 1/1/2013
• Preventing variceal bleeding in infants and children: Is less more?  
  Gastroenterology, 1/1/2013
• Liver transplantation for classical maple syrup urine disease: Long term follow-up in 37 patients and comparative UNOS experience  
  J Pediatr, 1/1/2012
• Congenital hepatic fibrosis and autosomal recessive polycystic kidney disease: An analytic review of the literature  
  J. Pediatr. Gastroenterol. Nutr., 1/1/2012
• Efficacy of fat soluble vitamin supplementation in infants with biliary atresia  
  Pediatrics, 1/1/2012
• Cross-sectional multi-center analysis of portal hypertension in 163 children and young adults with biliary atresia  
  J. Pediatr. Gastroenterol. Nutr, 1/1/2012
• Giant cell hepatitis and immune thrombocytopenic purpura-Reversal of liver failure with Rituximab therapy  
  J. Pediatr. Gastroenterol. Nutr, 1/1/2012
• To transplant or not to transplant-Certainly one of the questions  
  J. Pediatr. Gastroenterol. Nutr., 1/1/2012
• Diagnostic and therapeutic challenges in pediatric primary sclerosing cholangitis  
  Liver Transplantation, 1/1/2012
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Books/Book Chapters

• Nelson Textbook of Pediatrics 
  Chapter: Autoimmune Hepatitis 
  Editors: RM Kliegman, BF Stanton, JW St. Geme, NF Schor and RE Berman.Elsevier Saunders, Philadelphia, PAEdition 19th,2011
• Portal Hypertension V: Proceedings of the Fifth Baveno International Consensus Workshop 
  Chapter: Portal hypertension in children. Current practice and the need for evidence 
  Editors: R. de Franchis.Wiley-Blackwell, Hoboken, NJ2011
• Practical Gastroenterology and Hepatology, Liver and Biliary Disease 
  Chapter: Biliary atresia and cystic fibrosis: Transitioning care from pediatrics to internal medicine 
  Editors: N.J. Talley, K.D. Lindor and H.E. Vargas.Wiley-Blackwell, Hoboken, NJ2010
• The pediatric transplant manual 
  Chapter: Chronic liver disease and the pediatric patient 
  Editors: Remaley L, McGhee B, Reyes J, Mazariegos G.Lexi-Comp, Hudson, OH2009
• Walker's Pediatric Gastrointestinal Disease 
  BC Decker Publisher, Lewiston, NYEdition 5th,2008
• Bile Acids: Biological Actions and Clinical Relevance 
  Chapter: Regulation of intestinal bile acid transport in health and disease 
  Editors: U Beuers, D Keppler, L Leuschner, A Stiehl, and M Trauner.2007
• Physiology of the Gastrointestinal Tract 
  Chapter: Bile formation and the enterohepatic circulation of bile acids 
  Editors: L.R. Johnson.Edition 4th,2007
• Liver Disease in Children 
  Chapter: Familial Hepatocellular Cholestasis 
  Editors: F.J. Suchy, R.J. Sokol and W.F. Balistreri.Edition 3rd,2007
• Liver Disease in Children 
  Chapter: Portal Hypertension 
  Editors: F.J. Suchy, R.J. Sokol and W.F. Balistreri.Edition 3rd,2007
• Walker's Pediatric Gastrointestinal Disease 
  Chapter: Disorders of Biliary Transport 
  Editors: W.A. Walker, O.J. Goulet, R.E. Kleinman, P. Sherman, B.L. Shneider, I.R. Sanderson.BC Decker Publisher, Lewiston, NY2004
• Pediatric Gastrointestinal Disease 
  BC Decker Publisher, Lewiston, NYEdition 4th,2004
• Portal Hypertension in the 21st Century 
  Chapter: Approaches to the management of pediatric portal hypertension: Results of an informal survey 
  Editors: Groszmann R, Tygat N, Bosche J.Kluwer Academic Publishers, Boston, MA2004
• Nuclear Medicine in Clinical Diagnosis and Treatment 
  Chapter: Neonatal hyperbilirubinemia 
  Editors: Ell PJ and Gambhir SS.Churchill Livingstone, London, UKEdition 3rd,2004
• Rudolph's Pediatrics 
  Chapter: Metabolic Liver Disease 
  Editors: A.M. Rudolph and C.D. Rudolph.Edition 21st,2002
• The Pediatric Clinical Advisor 
  Chapter: Extrahepatic Biliary Atresia 
  Editors: L. Garfunkel, C. Christy and J. Kaczorowski.Harcourt, Inc2002
• Liver Disease in Children 
  2000
• Pediatric Gastrointestinal Disease:Pathophysiology, Diagnosis and Management 
  Chapter: Disorders of Biliary Transport 
  Editors: W.A. Walker, P.R. Durie, J.R. Hamilton, J.A. Walker-Smith, J.B. Watkins.Edition 3rd,2000
• Nelson's Textbook of Pediatrics 
  Chapter: Autoimmune (Chronic) Hepatitis 
  Editors: RE Berman.W.B. Saunders, Philadelphia, PAEdition 16th,1999
• Pediatric Gastrointestinal Disease: Pathophysiology, Diagnosis, Management 
  Chapter: Portal Hypertension 
  Editors: R. Wyllie and J. Hyams.W.B. Saunders, Philadelphia, PAEdition 2nd,1999
• Liver diseases in children 
  Chapter: Portal Hypertension 
  Editors: F Suchy.Mosby Year Book1995
• Gellis and Kagan's Current pediatric therapy 
  Chapter: Chronic active hepatitis 
  Editors: F Burg, J Ingelfinger and E Wald.W.B. SaundersEdition 14th,1993
• Liver and biliary diseases 
  Chapter: Neonatal jaundice and cholestasis 
  Editors: N. Kaplowitz.Williams and Wilkins1992
• Common problems in pediatric gastroenterology and nutrition 
  Chapter: Choledochal cysts 
  Editors: J Snyder and W Walker.Yearbook medical publishers1989
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Lectures

• Translational Investigations of Byler's Disease 
  Houston, TX - 1/16/2015
• Stratifying Risk and Individualizing Care for Portal Hypertenson- Controversies and Challenges in Pediatrics 
  Baveno, Italy - 1/11/2015
• Controversies in the Management of Varices in Children 
  Baveno, Italy - 1/11/2015
• Complexities in the Regulation of Intestinal Bile Acid Transport 
  Houston, TX - 1/5/2015
• Molecular Mechanisms of Intestinal Lipid Transport and Metabolism -Session Chair: Intestinal Bile Acid Metabolism, Regulation of the Intestinal Bile Acid Transporter a... 
  1/6/2014
• Biliary Atresia-Challenges and Opportunities 
  Children's Hospital of Pittsburgh of UPMC, Pittsburgh, PA - 1/6/2014
• Sociedade Portugesa de Gastroenterologia-Pediatric Portal Hypertension and Familial Cholestasis, Recent Advances in Molecular Mechanisms, Diagnosis and Management 
  Estoril, Portugal - 1/4/2014
• Primera jornada de Hepatologia infantil y transplante de higado pediatrico de la Fondacion Favaloro 
  Buenos Aires, Argentina - 1/31/2013
• PSC in Children: The Same Disease? 
  Pittsburgh, PA - 1/27/2013
• Neonatal Cholestasis and When to send children to a liver transplant center: Indications and controversies 
  Boston Children's Hospital, Cambridge, MA - 1/25/2013
• Liver Transplantation for Metabolic Disease: Complex Clinical Decision Making 
  Mount Sinai School of Medicine, New York, NY - 1/7/2013
• Liver Transplantation for Metabolic Disease: Traditional Indications 
  Barcelona, Spain - 1/5/2013
• Cholestasis in Pediatric Hepatology-Future Impact of Advances in Understanding Molecular Pathophysiology 
  Tokyo, Japan - 1/3/2013
• Hepatitis C and B in Children-Clinical Decision Making 
  West Virginia University, Morgantown, WV - 1/23/2012
• Rare Liver Diseases in Children 
  Westbrook, CT - 1/16/2012
• Management Controversies in Cystic Fibrosis Liver Disease 
  Boston, MA - 1/11/2012
• Molecular Diagnostics in Pediatric Hepatology and Evaluation of Neonatal Cholestasis 
  Bronx, NY - 1/7/2012
• Challenging the Paradigms: Liver Transplantation for Metabolic Disease 
  Pittsburgh, PA - 1/4/2012
• Familial Cholestasis, Molecular Mechansims, Diagnosis and Treatment 
  Institute of Liver and Biliary Sciences, Delhi, India - 1/21/2011
• Complexities in the Regulation of Ileal Bile Acid Transport 
  Pittsburgh, PA - 1/12/2011
• Approaches to the Management of Portal Hypertension in Children- Expert Pediatric Comentary on Baveno V 
  Pittsburgh, PA - 1/8/2011
• Familial Cholestasis, Molecular Mechanisms, Diagnosis and Treatment 
  ISMETT, Palermo, Italy - 1/6/2011
• Portal Hypertension in Children 
  San Francisco, CA - 1/5/2011
• Update on Pediatric Autoimmune Diseases-Diagnostic and Therapeutic Challenges in Pediatric Primary Sclerosing Cholangitis 
  San Francisco, CA - 1/4/2011
• Current Consensus and Future Directions in the Diagnosis and Treatment of Portal Hypertension - Portal Hypertension, Do the Rules Change in Children 
  Stresa, Italy - 1/22/2010
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Other

• ATP8B1 Deficiency. 
  GeneReviews
  University of Washington, Seattle, WA - 1/1/2009
• Low-gGT Familial Interhepatic Cholestasis 
  GeneReviews at GeneTests: Medical Genetics Information Resource
  http://www.genetests.org
  University of Washington, Seattle, WA - 1/1/2006
• Developmental aspects of hepatic bile acid transport. Proceedings of the 2nd Ringberg conference on cell biology and molecular basis of liver transport 
  Projekt
  Verlag, Dortmund - 1/1/1995