BenjaminShneiderMD

PubMed

• Educating pediatric gastroenterology fellows: Milestones, EPAs, & their application within a new educational curriculum.
  Kristin L Van Buren, Anna M Banc-Husu, Douglas S Fishman, Daniel H Leung, Benjamin L Shneider> ;Journal of Pediatric Gastroenterology and Nutrition. 2024 Apr 11
• Neonatal cholestasis in children with Alpha-1-AT deficiency is a risk for earlier severe liver disease with male predominance.
  Jeffrey Teckman, Philip Rosenthal, Rosalinda V Ignacio, Cathie Spino, Lee M Bass, Simon Horslen, Kasper Wang, John C Magee, Saul Karpen, Akihiro Asai, Jean P Molleston...> ;Hepatology Communications. 2023 Dec 1
• Sarcopenia is associated with osteopenia and impaired quality of life in children with genetic intrahepatic cholestatic liver disease.
  Julia M Boster, Nathan P Goodrich, Cathie Spino, Kathleen M Loomes, Estella M Alonso, Binita M Kamath, Ronald J Sokol, Saul Karpen, Alexander Miethke, Benjamin L Shnei...> ;Hepatology Communications. 2023 Nov 1
• The improving Medication Adherence in Adolescents and young adults following Liver Transplantation (iMALT) multisite trial: Design and trial implementation considerati...
  Eyal Shemesh, Sarah Duncan-Park, George Mazariegos, Rachel Annunziato, Ravinder Anand, Miguel Reyes-Mugica, Jeff Mitchell, Benjamin L Shneider> ;Clinical Trials. 2023 Oct 1
• 2 citations
  Characteristics of infections and their risk factors in children with biliary atresia.
  Henry Shiau, Jeremy M Schraw, Krupa Mysore, Laurel Cavallo, Sanjiv Harpavat, Philip J Lupo, Flor M Munoz, Benjamin L Shneider> ;Clinics and Research in Hepatology and Gastroenterology. 2023 Apr 1
• 4 citations
  Genotype-phenotype relationships of truncating mutations, p.E297G and p.D482G in bile salt export pump deficiency.
  Antonia Felzen, Daan B E van Wessel, Emmanuel Gonzales, Richard J Thompson, Irena Jankowska, Benjamin L Shneider, Etienne Sokal, Tassos Grammatikopoulos, Agustina Kada...> ;JHEP Reports. 2023 Feb 1
• Innate immune cell dysfunction and systemic inflammation in children with chronic liver diseases undergoing transplantation.
  Krupa R Mysore, Sunil Kannanganat, Jeremy M Schraw, Philip J Lupo, John A Goss, Kenneth D R Setchell, Farrah Kheradmand, Xian C Li, Benjamin L Shneider> ;American Journal of Transplantation. 2023 Jan 1
• Beyond Varices: Complications of Cirrhotic Portal Hypertension in Pediatrics.
  Anna M Banc-Husu, Henry Shiau, Peace Dike, Benjamin L Shneider> ;Seminars in Liver Disease. 2023 Feb 1
• 1 citations
  Assessment of telemedicine versus in-person care in managing abdominal pain in children during the COVID-19 pandemic.
  Amir Jazayeri, Julie V Dinh, Debra Eseonu, John M Hollier, Benjamin L Shneider> ;Journal of Telemedicine and Telecare. 2024 Apr 1
• 6 citations
  Serum bile acids as a prognostic biomarker in biliary atresia following Kasai portoenterostomy.
  Sanjiv Harpavat, Kieran Hawthorne, Kenneth D R Setchell, Monica Narvaez Rivas, Lisa Henn, Charlotte A Beil, Saul J Karpen, Vicky L Ng, Estella M Alonso, Jorge A Bezerr...> ;Hepatology. 2023 Mar 1
• 2 citations
  Serum biomarkers correlated with liver stiffness assessed in a multicenter study of pediatric cholestatic liver disease.
  Daniel H Leung, Sridevi Devaraj, Nathan P Goodrich, Xinpu Chen, Deepthi Rajapakshe, Wen Ye, Victor Andreev, Charles G Minard, Danielle Guffey, Jean P Molleston, Lee M ...> ;Hepatology. 2023 Feb 1
• 8 citations
  Risk of variceal hemorrhage and pretransplant mortality in children with biliary atresia.
  Lee M Bass, Wen Ye, Kieran Hawthorne, Daniel H Leung, Karen F Murray, Jean P Molleston, Rene Romero, Saul Karpen, Philip Rosenthal, Kathleen M Loomes, Kasper S Wang, R...> ;Hepatology. 2022 Sep 1
• 9 citations
  Impact of long-term administration of maralixibat on children with cholestasis secondary to Alagille syndrome.
  Shneider, B., Spino, C., Kamath, B., Magee, J., Ignacio, R., Huang, S., Horslen, S., Molleston, J., Miethke, A., Kohli, R., Leung, D., Jensen, M., Loomes, K., Karpen, ...> ;Hepatology Communications. 2022 Aug 1
• 3 citations
  Use of funded multicenter prospective longitudinal databases to inform clinical trials in rare diseases-Examination of cholestatic liver disease in Alagille syndrome.
  Benjamin L Shneider, Binita M Kamath, John C Magee, Nathan P Goodrich, Kathleen M Loomes, Wen Ye, Cathie Spino, Estella M Alonso, Jean P Molleston, Jorge A Bezerra, Ka...> ;Hepatology Communications. 2022 Aug 1
• 2 citations
  Fat Soluble Vitamin Assessment and Supplementation in Cholestasis.
  Binita M Kamath, Estella M Alonso, James E Heubi, Saul J Karpen, Shikha S Sundaram, Benjamin L Shneider, Ronald J Sokol> ;Clinics in Liver Disease. 2022 Aug 1
• 8 citations
  The Epidemiology of Biliary Atresia: Exploring the Role of Developmental Factors on Birth Prevalence.
  Laurel Cavallo, Erin M Kovar, Amal Aqul, Lucille McLoughlin, Naveen K Mittal, Norberto Rodriguez-Baez, Benjamin L Shneider, Robert J Zwiener, Tiffany M Chambers, Peter...> ;The Journal of Pediatrics. 2022 Jul 1
• 10 citations
  Newborn Screening for Biliary Atresia: a Review of Current Methods.
  Stephen L. Guthery, Ryan Himes, Benjamin L. Shneider, Sanjiv Harpavat> ;Current Gastroenterology Reports. 2021 Nov 24
• 4 citations
  Presentation and Outcomes of Infants With Idiopathic Cholestasis: A Multicenter Prospective Study.
  Paula M. Hertel, Kieran Hawthorne, Sehee Kim, Milton J. Finegold, Benjamin L. Shneider, James E. Squires, Nitika A. Gupta, Laura N. Bull, Karen F. Murray, Nanda Kerkar...> ;Journal of Pediatric Gastroenterology and Nutrition. 2021 Jul 23
• 7 citations
  Mutation Analysis and Disease Features at Presentation in a Multi-Center Cohort of Children With Monogenic Cholestasis.
  Heather van Doren, Paula M. Hertel, Laura N. Bull, Richard J. Thompson, Nathan P. Goodrich, Wen Ye, John C. Magee, Robert H. Squires, Lee M. Bass, James E. Heubi, Grac...> ;Journal of Pediatric Gastroenterology and Nutrition. 2021 May 13
• 7 citations
  Biomarkers for liver disease in urea cycle disorders.
  Sandesh C.S. Nagamani, Saima Ali, Rima Izem, Deborah Schady, Prakash Masand, Benjamin L. Shneider, Daniel H. Leung, Lindsay C. Burrage> ;Molecular Genetics and Metabolism. 2021 Apr 8
• 25 citations
  Impact of Genotype, Serum Bile Acids, and Surgical Biliary Diversion on Native Liver Survival in FIC1 Deficiency
  Daan B E van Wessel, Richard J. Thompson, Emmanuel Gonzales, Irena Jankowska, Benjamin L. Shneider, Etienne Sokal, Tassos Grammatikopoulos, Agustina Kadaristiana, Emma...> ;Hepatology. 2021 Mar 5
• 1 citations
  Constitutive activation of mitogen-activated protein kinase kinase (MEK1) in ileal enterocytes leads to dysplasia and a predisposition to cancer
  Benjamin L. Shneider, Nahir Cortes-Santiago, Deborah Schady, Swapna Krishnamoorthy, Sundararajah Thevananther, Kimal Rajapakshe, Dimuthu Perera, Shixia Huang, Cristian...> ;American Journal of Physiology. Gastrointestinal and Liver Physiology. 2021 Mar 1
• 2 citations
  Approaches to Research Determination of Late Acute Cellular Rejection in Pediatric Liver Transplant Recipients.
  George V. Mazariegos, Benjamin L. Shneider, Eyal Shemesh, Deborah Schady, Hector Melin-Aldana, Soo-Jin Cho, Ravinder Anand, Jinson Erinjeri, Rachel A. Annunziato, Migu...> ;Liver Transplantation. 2021 Jan 1
• 1 citations
  Operational Definitions for Chronic Liver Disease Manifestations and Recurring Clinical Events in Biliary Atresia.
  Henry Shiau, Jeremy M. Schraw, Laurel Cavallo, Daniel H. Leung, Sanjiv Harpavat, Philip J. Lupo, Benjamin L. Shneider> ;Journal of Pediatric Gastroenterology and Nutrition. 2021 Apr 1
• 5 citations
  Longitudinal Outcomes in Young Patients with Alpha-1-Antitrypsin Deficiency with Native Liver Reveal that Neonatal Cholestasis is a Poor Predictor of Future Portal Hyp...
  Jeffrey Teckman, Philip J. Rosenthal, Kieran Hawthorne, Cathie Spino, Lee M. Bass, Karen F. Murray, Nanda Kerkar, John C. Magee, Saul J. Karpen, James E. Heubi, Jean P...> ;The Journal of Pediatrics. 2020 Dec 1
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Journal Articles

• Accuracy of the Pediatric End-Stage Liver Disease Score in Estimating Pretransplant Mortality Among Pediatric Liver Transplant Candidates  
  Robert H Squires, Benjamin L Shneider, JAMA
• Bile acid pool dynamics in progressive familial intrahepatic cholestasis with partial external biliary diversion  
  J. Pediatr. Gastroenterol. Nutr, 1/1/2015
• Byler's Disease-Early natural history, A single center case series  
  J. Pediatr. Gastroenterol. Nutr, 1/1/2015
• c-Fos mediates repression of the apical sodium dependent bile acid transporter by fibroblast growth factor-19 in mice  
  Am. J. Physiol.: GI and Liver, 1/1/2014
• Effect of high dose corticosteroids following hepatoportoenterostomy on bile drainage in infants with biliary atresia: The START randomized clinical trial  
  JAMA, 1/1/2014
• Medical status of 219 children with biliary atresia surviving long-term with their native livers: Results of a North American multicenter consortium  
  J. Pediatr., 1/1/2014
• The Medication Level Variability Index (MLVI) predicts rejection, possibly due to nonadherence, in adult liver transplant recipients  
  Liver Transplantation, 1/1/2014
• A single element in the 3'UTR of the Apical Sodium-Dependent Bile Acid Transporter controls both stabilization and destabilization of mRNA  
  Biochemical Journal, 1/1/2014
• Total serum bilirubin predicts fat-soluble vitamin deficiency better than serum bile acids in infants with biliary atresia  
  J. Pediatr. Gastroenterol. Nutr, 1/1/2014
• Liver transplantation for pediatric metabolic disease  
  Molec. Genet. Metabol, 1/1/2014
• Autosomal recessive polycystic kidney disease: Report of an international clinical care conference  
  J. Pediatr, 1/1/2014
• Delta4-3-oxosteroid 5beta-reductase deficiency causing neonatal liver failure and hemochromatosis  
  J Ped, 1/1/2014
• King's College Hospital criteria for nonacetaminophen induced acute liver failure in an international cohort of children  
  J. Pediatr, 1/1/2013
• Intravenous N-acetylcysteine in pediatric patients with non-acetaminophen acute liver failure: A placebo-controlled clinical trial  
  Hepatology, 1/1/2013
• Phospholipase D2 mediates signaling by ATPase Class I Type 8B Membrane 1  
  J. Lipid Res, 1/1/2013
• Liver Transplantation for children with biliary atresia in the PELD era: Role of insurance status  
  Liver Transplantation, 1/1/2013
• Extra-hepatic anomalies in infants with biliary atresia: Results of a large prospective North American multi-center study  
  Hepatology, 1/1/2013
• Preventing variceal bleeding in infants and children: Is less more?  
  Gastroenterology, 1/1/2013
• Liver transplantation for classical maple syrup urine disease: Long term follow-up in 37 patients and comparative UNOS experience  
  J Pediatr, 1/1/2012
• Congenital hepatic fibrosis and autosomal recessive polycystic kidney disease: An analytic review of the literature  
  J. Pediatr. Gastroenterol. Nutr., 1/1/2012
• Efficacy of fat soluble vitamin supplementation in infants with biliary atresia  
  Pediatrics, 1/1/2012
• Cross-sectional multi-center analysis of portal hypertension in 163 children and young adults with biliary atresia  
  J. Pediatr. Gastroenterol. Nutr, 1/1/2012
• Giant cell hepatitis and immune thrombocytopenic purpura-Reversal of liver failure with Rituximab therapy  
  J. Pediatr. Gastroenterol. Nutr, 1/1/2012
• To transplant or not to transplant-Certainly one of the questions  
  J. Pediatr. Gastroenterol. Nutr., 1/1/2012
• Diagnostic and therapeutic challenges in pediatric primary sclerosing cholangitis  
  Liver Transplantation, 1/1/2012
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Books/Book Chapters

• Portal Hypertension V: Proceedings of the Fifth Baveno International Consensus Workshop 
  Chapter: Portal hypertension in children. Current practice and the need for evidence 
  Editors: R. de Franchis.Wiley-Blackwell, Hoboken, NJ2011
• Nelson Textbook of Pediatrics 
  Chapter: Autoimmune Hepatitis 
  Editors: RM Kliegman, BF Stanton, JW St. Geme, NF Schor and RE Berman.Elsevier Saunders, Philadelphia, PAEdition 19th,2011
• Practical Gastroenterology and Hepatology, Liver and Biliary Disease 
  Chapter: Biliary atresia and cystic fibrosis: Transitioning care from pediatrics to internal medicine 
  Editors: N.J. Talley, K.D. Lindor and H.E. Vargas.Wiley-Blackwell, Hoboken, NJ2010
• The pediatric transplant manual 
  Chapter: Chronic liver disease and the pediatric patient 
  Editors: Remaley L, McGhee B, Reyes J, Mazariegos G.Lexi-Comp, Hudson, OH2009
• Walker's Pediatric Gastrointestinal Disease 
  BC Decker Publisher, Lewiston, NYEdition 5th,2008
• Liver Disease in Children 
  Chapter: Portal Hypertension 
  Editors: F.J. Suchy, R.J. Sokol and W.F. Balistreri.Edition 3rd,2007
• Liver Disease in Children 
  Chapter: Familial Hepatocellular Cholestasis 
  Editors: F.J. Suchy, R.J. Sokol and W.F. Balistreri.Edition 3rd,2007
• Physiology of the Gastrointestinal Tract 
  Chapter: Bile formation and the enterohepatic circulation of bile acids 
  Editors: L.R. Johnson.Edition 4th,2007
• Bile Acids: Biological Actions and Clinical Relevance 
  Chapter: Regulation of intestinal bile acid transport in health and disease 
  Editors: U Beuers, D Keppler, L Leuschner, A Stiehl, and M Trauner.2007
• Nuclear Medicine in Clinical Diagnosis and Treatment 
  Chapter: Neonatal hyperbilirubinemia 
  Editors: Ell PJ and Gambhir SS.Churchill Livingstone, London, UKEdition 3rd,2004
• Walker's Pediatric Gastrointestinal Disease 
  Chapter: Disorders of Biliary Transport 
  Editors: W.A. Walker, O.J. Goulet, R.E. Kleinman, P. Sherman, B.L. Shneider, I.R. Sanderson.BC Decker Publisher, Lewiston, NY2004
• Portal Hypertension in the 21st Century 
  Chapter: Approaches to the management of pediatric portal hypertension: Results of an informal survey 
  Editors: Groszmann R, Tygat N, Bosche J.Kluwer Academic Publishers, Boston, MA2004
• Pediatric Gastrointestinal Disease 
  BC Decker Publisher, Lewiston, NYEdition 4th,2004
• The Pediatric Clinical Advisor 
  Chapter: Extrahepatic Biliary Atresia 
  Editors: L. Garfunkel, C. Christy and J. Kaczorowski.Harcourt, Inc2002
• Rudolph's Pediatrics 
  Chapter: Metabolic Liver Disease 
  Editors: A.M. Rudolph and C.D. Rudolph.Edition 21st,2002
• Pediatric Gastrointestinal Disease:Pathophysiology, Diagnosis and Management 
  Chapter: Disorders of Biliary Transport 
  Editors: W.A. Walker, P.R. Durie, J.R. Hamilton, J.A. Walker-Smith, J.B. Watkins.Edition 3rd,2000
• Liver Disease in Children 
  2000
• Pediatric Gastrointestinal Disease: Pathophysiology, Diagnosis, Management 
  Chapter: Portal Hypertension 
  Editors: R. Wyllie and J. Hyams.W.B. Saunders, Philadelphia, PAEdition 2nd,1999
• Nelson's Textbook of Pediatrics 
  Chapter: Autoimmune (Chronic) Hepatitis 
  Editors: RE Berman.W.B. Saunders, Philadelphia, PAEdition 16th,1999
• Liver diseases in children 
  Chapter: Portal Hypertension 
  Editors: F Suchy.Mosby Year Book1995
• Gellis and Kagan's Current pediatric therapy 
  Chapter: Chronic active hepatitis 
  Editors: F Burg, J Ingelfinger and E Wald.W.B. SaundersEdition 14th,1993
• Liver and biliary diseases 
  Chapter: Neonatal jaundice and cholestasis 
  Editors: N. Kaplowitz.Williams and Wilkins1992
• Common problems in pediatric gastroenterology and nutrition 
  Chapter: Choledochal cysts 
  Editors: J Snyder and W Walker.Yearbook medical publishers1989
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Lectures

• Translational Investigations of Byler's Disease 
  Houston, TX - 1/16/2015
• Stratifying Risk and Individualizing Care for Portal Hypertenson- Controversies and Challenges in Pediatrics 
  Baveno, Italy - 1/11/2015
• Controversies in the Management of Varices in Children 
  Baveno, Italy - 1/11/2015
• Complexities in the Regulation of Intestinal Bile Acid Transport 
  Houston, TX - 1/5/2015
• Molecular Mechanisms of Intestinal Lipid Transport and Metabolism -Session Chair: Intestinal Bile Acid Metabolism, Regulation of the Intestinal Bile Acid Transporter a... 
  1/6/2014
• Biliary Atresia-Challenges and Opportunities 
  Children's Hospital of Pittsburgh of UPMC, Pittsburgh, PA - 1/6/2014
• Sociedade Portugesa de Gastroenterologia-Pediatric Portal Hypertension and Familial Cholestasis, Recent Advances in Molecular Mechanisms, Diagnosis and Management 
  Estoril, Portugal - 1/4/2014
• Primera jornada de Hepatologia infantil y transplante de higado pediatrico de la Fondacion Favaloro 
  Buenos Aires, Argentina - 1/31/2013
• PSC in Children: The Same Disease? 
  Pittsburgh, PA - 1/27/2013
• Neonatal Cholestasis and When to send children to a liver transplant center: Indications and controversies 
  Boston Children's Hospital, Cambridge, MA - 1/25/2013
• Liver Transplantation for Metabolic Disease: Complex Clinical Decision Making 
  Mount Sinai School of Medicine, New York, NY - 1/7/2013
• Liver Transplantation for Metabolic Disease: Traditional Indications 
  Barcelona, Spain - 1/5/2013
• Cholestasis in Pediatric Hepatology-Future Impact of Advances in Understanding Molecular Pathophysiology 
  Tokyo, Japan - 1/3/2013
• Hepatitis C and B in Children-Clinical Decision Making 
  West Virginia University, Morgantown, WV - 1/23/2012
• Rare Liver Diseases in Children 
  Westbrook, CT - 1/16/2012
• Management Controversies in Cystic Fibrosis Liver Disease 
  Boston, MA - 1/11/2012
• Molecular Diagnostics in Pediatric Hepatology and Evaluation of Neonatal Cholestasis 
  Bronx, NY - 1/7/2012
• Challenging the Paradigms: Liver Transplantation for Metabolic Disease 
  Pittsburgh, PA - 1/4/2012
• Familial Cholestasis, Molecular Mechansims, Diagnosis and Treatment 
  Institute of Liver and Biliary Sciences, Delhi, India - 1/21/2011
• Complexities in the Regulation of Ileal Bile Acid Transport 
  Pittsburgh, PA - 1/12/2011
• Approaches to the Management of Portal Hypertension in Children- Expert Pediatric Comentary on Baveno V 
  Pittsburgh, PA - 1/8/2011
• Familial Cholestasis, Molecular Mechanisms, Diagnosis and Treatment 
  ISMETT, Palermo, Italy - 1/6/2011
• Portal Hypertension in Children 
  San Francisco, CA - 1/5/2011
• Update on Pediatric Autoimmune Diseases-Diagnostic and Therapeutic Challenges in Pediatric Primary Sclerosing Cholangitis 
  San Francisco, CA - 1/4/2011
• Current Consensus and Future Directions in the Diagnosis and Treatment of Portal Hypertension - Portal Hypertension, Do the Rules Change in Children 
  Stresa, Italy - 1/22/2010
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Other

• ATP8B1 Deficiency. 
  GeneReviews
  University of Washington, Seattle, WA - 1/1/2009
• Low-gGT Familial Interhepatic Cholestasis 
  GeneReviews at GeneTests: Medical Genetics Information Resource
  http://www.genetests.org
  University of Washington, Seattle, WA - 1/1/2006
• Developmental aspects of hepatic bile acid transport. Proceedings of the 2nd Ringberg conference on cell biology and molecular basis of liver transport 
  Projekt
  Verlag, Dortmund - 1/1/1995